Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Br J Haematol ;93 2: This explains the discrepancy between these values. Aires, Argentina; 16 2: Servicio de ayuda de la revista.

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Se recomienda el monitoreo de glucemia y ferritina. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis. Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Splenectomy for hereditary spherocytosis: Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis.


J Lab Clin Med. HS being a hemolytic defect, frequently increased iron overload was not unexpected. Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare. Bienvenido a siicsalud Contacto Inquietudes.

Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis.

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Int J Pediatr Hematol Oncol ; 2: King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis. Oxygen affinity and compensated hemolysis in hereditary spherocytosis. Revista Cubana Hematol Inmunol Hemoter ;18 1: Blood Cells Mol Dis ; Este hecho explica la discrepancia entre estos valores.

Journal of Medical Cases.

Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both volume and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements. Monitoring of blood glucose and ferritin is esfrrocitosis. Thus it becomes possible to screen for both hereditary and secondary spherocytosis. Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms.


The Italian survey on hereditary spherocytosis. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: A study of 62 Spanish cases. Referencias -Mayelin Herrera Garcia. Hereditary Spherocytosis in Neonates esferocitpsis Hyperbilirubinemia.

Polish Academjy of Sciences? Erythroid membrane protein defects in hereditary spherocytosis.

Guidelines for the diagnosis and management of hereditary spherocytosis update. The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established. Clinico-hematological profile of hereditary spherocytosis: Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of 1: De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria.

J Thromb Thrombolysis ;17 3: Am J Hematol ;57 1: